Abstract
Unique socio-behavioural phenotypes are reported for individuals with different neurodevelopmental disorders. Here, the effects of adult familiarity and nature of interaction on social anxiety and social motivation were investigated in individuals with fragile X (FXS; n = 20), Cornelia de Lange (CdLS; n = 20) and Rubinstein-Taybi (RTS; n = 20) syndromes, compared to individuals with Down syndrome (DS; n = 20). The Social Anxiety and Motivation Rating Scale was employed whilst participants completed four social tasks, each administered separately by a familiar adult, and also by an unfamiliar adult. Compared to participants with DS, those with FXS and RTS exhibited high levels of social anxiety but similar levels of social motivation. Participants with CdLS showed heightened social anxiety and reduced social motivation only during interactions with an unfamiliar adult when active participation was voluntary.
Original language | English |
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Pages (from-to) | 127-144 |
Number of pages | 18 |
Journal | Journal of Autism and Developmental Disorders |
Volume | 50 |
Issue number | 1 |
Early online date | 21 Sept 2019 |
DOIs | |
Publication status | Published - Jan 2020 |
Funder
Economic and Social Research council (Grant Number: ES/I901825/1) and by CerebraFunding
The authors would like to thank all participants and their families. The authors are indebted to the Fragile X Society, the Cornelia de Lange Foundation UK & Ireland, and the Rubinstein-Taybi Syndrome Support Group for their assistance with recruitment of participants. This study was funded by a grant from the Economic and Social Research council (Grant Number: ES/I901825/1) and by Cerebra.
Funders | Funder number |
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Cornelia de Lange Syndrome Foundation | |
Rubinstein-Taybi Syndrome Support Group | |
Economic and Social Research Council | ES/I901825/1 |
Keywords
- Cornelia de Lange syndrome
- Down syndrome
- Fragile X syndrome
- Rubinstein-Taybi syndrome
- Social anxiety
- social motivation
ASJC Scopus subject areas
- Developmental and Educational Psychology